Sfoglia per Autore
Impact of R4496C RyR2 mutation on myocardial contractility
2011 Raffaele Coppini; Cecilia Ferrantini; Claudia Ferrara; Beatrice Scellini; Francesca Stillitano; Chiara Tesi; Elisabetta Cerbai; Silvia Priori; Corrado Poggesi
The HCM-Associated Cardiac Troponin T Mutation K273N Accelerates Tension Generation and Relaxation in Human Cardiac Myofibrils
2011 Claudia Ferrara; Nicoletta Piroddi; Beatrice Scellini; Cecilia Ferrantini; Sabine J. van Dijk; Cris dos Remedios; Chiara Tesi; Jolanda van der Velden; Corrado Poggesi
Age-related decline in contractile function of ventricular myofibrils from HCM patients carrying MYBPC3 mutations
2011 Ferrantini C.; Belus A.; Piroddi N.; Ferrara C.; Scellini B.; Tesi C.; Cecchi F.; Olivotto I.; Poggesi C.
Novel method of obtaining myofibrils from cardiomyocyte cultures
2012 Jeong M.; Ferrara C.; Ferrantini C.; Coppini R.; Scellini B.; Piroddi N.; Tesi C.; Cerbai E.; Poggesi C.
The HCM-associated cardiac Troponin T mutation K280N accelerates tension generation and relaxation in human cardiac myofibrils
2012 Ferrara C; Piroddi N; Scellini B; Ferrantini C; Sequiera V; Remedios C; Carrier L; Tesi C ; Van Der Velden J; Poggesi C.
Tropomyosin D137L of reduced flexibility increases submaximal calcium-activated tension in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution
2012 Beatrice Scellini; Claudia Ferrara; Nicoletta Piroddi; John Sumida; Corrado Poggesi; Sherwin S. Lehrer; Chiara Tesi
Tropomyosin flexibility modulates Ca2+ sensitivity of thin filament and affects tension relaxation in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution
2012 Scellini B.; Ferrara C.; Piroddi N.; Sumida J.; Poggesi C.; Lehrer S.S.; Tesi C.
The HCM-associated cardiac Troponin T mutation K280N increases the energetic cost of tension generation in human cardiac myofibrils
2013 Ferrara C.; Witjas-Paalberends R.; Piroddi N.; Scellini B.; Tesi C.; Sequiera V.; dos Remedios C.; Schlossarek S.; Leung J; Carrier L.; Redwood C.; Marston S.; van der Velden J.; Poggesi C.
Impact of sarcomeric protein mutations associated to myopathies on the mechanics and energetics of myofibril contraction
2013 Claudia Ferrara
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy
2013 Ottenheijm, Cac; Buck, D; de Winter, J; Ferrara, Claudia; Piroddi, Nicoletta; Tesi, Chiara; Jasper, R; Malik, F; Meng, F; Stienen, G; Beggs, Ah; Labeit, S; Poggesi, Corrado; Lawlor, M; Granzier, H.
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy
2013 Ottenheijm CA; Buck D; de Winter JM; Ferrara C; Piroddi N; Tesi C; Jasper JR; Malik FI; Meng H; Stienen GJ; Beggs AH; Labeit S; Poggesi C; Lawlor MW; Granzier H
Altered Cross Bridge Kinetics in Skeletal Myofibrils from NEBDex55, a Novel Mouse Model of Nebulin-Based Nemaline Myopathy
2013 Ferrara, Claudia; Buck, Danielle; Piroddi, Nicoletta; Tesi, Chiara; LeWinter, Josine; Ottenheijm, Coen; Poggesi, Corrado; Granzier, Henk
Mutations in MYH7 reduce the force generating capacity of sarcomeres in human familial hypertrophic cardiomyopathy.
2013 Witjas-Paalberends ER; Piroddi N; Stam K; van Dijk SJ; Oliviera VS; Ferrara C; Scellini B; Hazebroek M; Ten Cate FJ; van Slegtenhorst M; Dos Remedios C; Niessen HW; Tesi C; Stienen GJ; Heymans S; Michels M; Poggesi C; van der Velden J.
Faster cross-bridge detachment and increased tension cost in human hypertrophic cardiomyopathy with the R403Q MYH7 mutation
2014 Witjas-Paalberends ER; Ferrara C; Scellini B; Piroddi N; Montag J; Tesi C; Stienen GJ; Michels M; Ho CY; Kraft T; Poggesi C; van der Velden J.
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model
2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q Myh7 Mutation
2014 Witjas-Paalberends R.; Ferrara C.; Scellini B.; Montag J.; Stienen G.; Kraft T.; Michels M.; Ho C.; Poggesi C.; van der Velden J.
HDAC6 contributes to pathological responses of heart and skeletal muscle to chronic angiotensin-II signaling.
2014 Demos-Davies KM; Ferguson BS; Cavasin MA; Mahaffey JH; Williams SM; Spiltoir JI; Schuetze KB; Horn TR; Chen B; Ferrara C; Scellini B; Piroddi N; Tesi C; Poggesi C; Jeong MY; McKinsey TA
Mutations in the central part of a Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after troponin–tropomyosin removal and reconstitution
2015 Beatrice, Scellini; Nicoletta, Piroddi; Claudia, Ferrara; Matyushenko, Alexander; Levitsky, Dmitrii; Corrado, Poggesi; Chiara, Tesi
R4496C RyR2 mutation impairs atrial and ventricular contractility
2016 Ferrantini, Cecilia; Coppini, Raffaele; Scellini, Beatrice; Ferrara, Claudia; Pioner, Josè Manuel; Mazzoni, Luca; Priori, Silvia; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado
The homozygous K280N troponin T mutation alters cross-bridge kinetics and energetics in human HCM
2019 Piroddi, Nicoletta; Witjas-Paalberends, E. Rosalie; Ferrara, Claudia; Ferrantini, Cecilia; Vitale, Giulia; Scellini, Beatrice; Wijnker, Paul J.M.; Sequiera, Vasco; Dooijes, Dennis; dos Remedios, Cristobal; Schlossarek, Saskia; Leung, Man Ching; Messer, Andrew; Ward, Douglas G.; Biggeri, Annibale; Tesi, Chiara; Carrier, Lucie; Redwood, Charles S.; Marston, Steven B.; van der Velden, Jolanda; Poggesi, Corrado
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Impact of R4496C RyR2 mutation on myocardial contractility | 2011 | Raffaele Coppini; Cecilia Ferrantini; Claudia Ferrara; Beatrice Scellini; Francesca Stillitano; Chiara Tesi; Elisabetta Cerbai; Silvia Priori; Corrado Poggesi | |
The HCM-Associated Cardiac Troponin T Mutation K273N Accelerates Tension Generation and Relaxation in Human Cardiac Myofibrils | 2011 | Claudia Ferrara; Nicoletta Piroddi; Beatrice Scellini; Cecilia Ferrantini; Sabine J. van Dijk; Cris dos Remedios; Chiara Tesi; Jolanda van der Velden; Corrado Poggesi | |
Age-related decline in contractile function of ventricular myofibrils from HCM patients carrying MYBPC3 mutations | 2011 | Ferrantini C.; Belus A.; Piroddi N.; Ferrara C.; Scellini B.; Tesi C.; Cecchi F.; Olivotto I.; Poggesi C. | |
Novel method of obtaining myofibrils from cardiomyocyte cultures | 2012 | Jeong M.; Ferrara C.; Ferrantini C.; Coppini R.; Scellini B.; Piroddi N.; Tesi C.; Cerbai E.; Poggesi C. | |
The HCM-associated cardiac Troponin T mutation K280N accelerates tension generation and relaxation in human cardiac myofibrils | 2012 | Ferrara C; Piroddi N; Scellini B; Ferrantini C; Sequiera V; Remedios C; Carrier L; Tesi C ; Van Der Velden J; Poggesi C. | |
Tropomyosin D137L of reduced flexibility increases submaximal calcium-activated tension in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution | 2012 | Beatrice Scellini; Claudia Ferrara; Nicoletta Piroddi; John Sumida; Corrado Poggesi; Sherwin S. Lehrer; Chiara Tesi | |
Tropomyosin flexibility modulates Ca2+ sensitivity of thin filament and affects tension relaxation in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution | 2012 | Scellini B.; Ferrara C.; Piroddi N.; Sumida J.; Poggesi C.; Lehrer S.S.; Tesi C. | |
The HCM-associated cardiac Troponin T mutation K280N increases the energetic cost of tension generation in human cardiac myofibrils | 2013 | Ferrara C.; Witjas-Paalberends R.; Piroddi N.; Scellini B.; Tesi C.; Sequiera V.; dos Remedios C.; Schlossarek S.; Leung J; Carrier L.; Redwood C.; Marston S.; van der Velden J.; Poggesi C. | |
Impact of sarcomeric protein mutations associated to myopathies on the mechanics and energetics of myofibril contraction | 2013 | Claudia Ferrara | |
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy | 2013 | Ottenheijm, Cac; Buck, D; de Winter, J; Ferrara, Claudia; Piroddi, Nicoletta; Tesi, Chiara; Jasper, R; Malik, F; Meng, F; Stienen, G; Beggs, Ah; Labeit, S; Poggesi, Corrado; Lawlor, M; Granzier, H. | |
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy | 2013 | Ottenheijm CA; Buck D; de Winter JM; Ferrara C; Piroddi N; Tesi C; Jasper JR; Malik FI; Meng H; Stienen GJ; Beggs AH; Labeit S; Poggesi C; Lawlor MW; Granzier H | |
Altered Cross Bridge Kinetics in Skeletal Myofibrils from NEBDex55, a Novel Mouse Model of Nebulin-Based Nemaline Myopathy | 2013 | Ferrara, Claudia; Buck, Danielle; Piroddi, Nicoletta; Tesi, Chiara; LeWinter, Josine; Ottenheijm, Coen; Poggesi, Corrado; Granzier, Henk | |
Mutations in MYH7 reduce the force generating capacity of sarcomeres in human familial hypertrophic cardiomyopathy. | 2013 | Witjas-Paalberends ER; Piroddi N; Stam K; van Dijk SJ; Oliviera VS; Ferrara C; Scellini B; Hazebroek M; Ten Cate FJ; van Slegtenhorst M; Dos Remedios C; Niessen HW; Tesi C; Stienen GJ; Heymans S; Michels M; Poggesi C; van der Velden J. | |
Faster cross-bridge detachment and increased tension cost in human hypertrophic cardiomyopathy with the R403Q MYH7 mutation | 2014 | Witjas-Paalberends ER; Ferrara C; Scellini B; Piroddi N; Montag J; Tesi C; Stienen GJ; Michels M; Ho CY; Kraft T; Poggesi C; van der Velden J. | |
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model | 2014 | Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C. | |
Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q Myh7 Mutation | 2014 | Witjas-Paalberends R.; Ferrara C.; Scellini B.; Montag J.; Stienen G.; Kraft T.; Michels M.; Ho C.; Poggesi C.; van der Velden J. | |
HDAC6 contributes to pathological responses of heart and skeletal muscle to chronic angiotensin-II signaling. | 2014 | Demos-Davies KM; Ferguson BS; Cavasin MA; Mahaffey JH; Williams SM; Spiltoir JI; Schuetze KB; Horn TR; Chen B; Ferrara C; Scellini B; Piroddi N; Tesi C; Poggesi C; Jeong MY; McKinsey TA | |
Mutations in the central part of a Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after troponin–tropomyosin removal and reconstitution | 2015 | Beatrice, Scellini; Nicoletta, Piroddi; Claudia, Ferrara; Matyushenko, Alexander; Levitsky, Dmitrii; Corrado, Poggesi; Chiara, Tesi | |
R4496C RyR2 mutation impairs atrial and ventricular contractility | 2016 | Ferrantini, Cecilia; Coppini, Raffaele; Scellini, Beatrice; Ferrara, Claudia; Pioner, Josè Manuel; Mazzoni, Luca; Priori, Silvia; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado | |
The homozygous K280N troponin T mutation alters cross-bridge kinetics and energetics in human HCM | 2019 | Piroddi, Nicoletta; Witjas-Paalberends, E. Rosalie; Ferrara, Claudia; Ferrantini, Cecilia; Vitale, Giulia; Scellini, Beatrice; Wijnker, Paul J.M.; Sequiera, Vasco; Dooijes, Dennis; dos Remedios, Cristobal; Schlossarek, Saskia; Leung, Man Ching; Messer, Andrew; Ward, Douglas G.; Biggeri, Annibale; Tesi, Chiara; Carrier, Lucie; Redwood, Charles S.; Marston, Steven B.; van der Velden, Jolanda; Poggesi, Corrado |
Legenda icone
- file ad accesso aperto
- file disponibili sulla rete interna
- file disponibili agli utenti autorizzati
- file disponibili solo agli amministratori
- file sotto embargo
- nessun file disponibile