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Impact of R4496C RyR2 mutation on myocardial contractility 2011 Raffaele Coppini; Cecilia Ferrantini; Claudia Ferrara; Beatrice Scellini; Francesca Stillitano; Chiara Tesi; Elisabetta Cerbai; Silvia Priori; Corrado Poggesi
The HCM-Associated Cardiac Troponin T Mutation K273N Accelerates Tension Generation and Relaxation in Human Cardiac Myofibrils 2011 Claudia Ferrara; Nicoletta Piroddi; Beatrice Scellini; Cecilia Ferrantini; Sabine J. van Dijk; Cris dos Remedios; Chiara Tesi; Jolanda van der Velden; Corrado Poggesi
Age-related decline in contractile function of ventricular myofibrils from HCM patients carrying MYBPC3 mutations 2011 Ferrantini C.; Belus A.; Piroddi N.; Ferrara C.; Scellini B.; Tesi C.; Cecchi F.; Olivotto I.; Poggesi C.
Novel method of obtaining myofibrils from cardiomyocyte cultures 2012 Jeong M.; Ferrara C.; Ferrantini C.; Coppini R.; Scellini B.; Piroddi N.; Tesi C.; Cerbai E.; Poggesi C.
The HCM-associated cardiac Troponin T mutation K280N accelerates tension generation and relaxation in human cardiac myofibrils 2012 Ferrara C; Piroddi N; Scellini B; Ferrantini C; Sequiera V; Remedios C; Carrier L; Tesi C ; Van Der Velden J; Poggesi C.
Tropomyosin D137L of reduced flexibility increases submaximal calcium-activated tension in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution 2012 Beatrice Scellini; Claudia Ferrara; Nicoletta Piroddi; John Sumida; Corrado Poggesi; Sherwin S. Lehrer; Chiara Tesi
Tropomyosin flexibility modulates Ca2+ sensitivity of thin filament and affects tension relaxation in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution 2012 Scellini B.; Ferrara C.; Piroddi N.; Sumida J.; Poggesi C.; Lehrer S.S.; Tesi C.
The HCM-associated cardiac Troponin T mutation K280N increases the energetic cost of tension generation in human cardiac myofibrils 2013 Ferrara C.; Witjas-Paalberends R.; Piroddi N.; Scellini B.; Tesi C.; Sequiera V.; dos Remedios C.; Schlossarek S.; Leung J; Carrier L.; Redwood C.; Marston S.; van der Velden J.; Poggesi C.
Impact of sarcomeric protein mutations associated to myopathies on the mechanics and energetics of myofibril contraction 2013 Claudia Ferrara
Altered Cross Bridge Kinetics in Skeletal Myofibrils from NEBDex55, a Novel Mouse Model of Nebulin-Based Nemaline Myopathy 2013 Ferrara, Claudia; Buck, Danielle; Piroddi, Nicoletta; Tesi, Chiara; LeWinter, Josine; Ottenheijm, Coen; Poggesi, Corrado; Granzier, Henk
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy 2013 Ottenheijm CA; Buck D; de Winter JM; Ferrara C; Piroddi N; Tesi C; Jasper JR; Malik FI; Meng H; Stienen GJ; Beggs AH; Labeit S; Poggesi C; Lawlor MW; Granzier H
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy 2013 Ottenheijm, Cac; Buck, D; de Winter, J; Ferrara, Claudia; Piroddi, Nicoletta; Tesi, Chiara; Jasper, R; Malik, F; Meng, F; Stienen, G; Beggs, Ah; Labeit, S; Poggesi, Corrado; Lawlor, M; Granzier, H.
Mutations in MYH7 reduce the force generating capacity of sarcomeres in human familial hypertrophic cardiomyopathy. 2013 Witjas-Paalberends ER; Piroddi N; Stam K; van Dijk SJ; Oliviera VS; Ferrara C; Scellini B; Hazebroek M; Ten Cate FJ; van Slegtenhorst M; Dos Remedios C; Niessen HW; Tesi C; Stienen GJ; Heymans S; Michels M; Poggesi C; van der Velden J.
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model 2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
HDAC6 contributes to pathological responses of heart and skeletal muscle to chronic angiotensin-II signaling. 2014 Demos-Davies KM; Ferguson BS; Cavasin MA; Mahaffey JH; Williams SM; Spiltoir JI; Schuetze KB; Horn TR; Chen B; Ferrara C; Scellini B; Piroddi N; Tesi C; Poggesi C; Jeong MY; McKinsey TA
Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q Myh7 Mutation 2014 Witjas-Paalberends R.; Ferrara C.; Scellini B.; Montag J.; Stienen G.; Kraft T.; Michels M.; Ho C.; Poggesi C.; van der Velden J.
Faster cross-bridge detachment and increased tension cost in human hypertrophic cardiomyopathy with the R403Q MYH7 mutation 2014 Witjas-Paalberends ER; Ferrara C; Scellini B; Piroddi N; Montag J; Tesi C; Stienen GJ; Michels M; Ho CY; Kraft T; Poggesi C; van der Velden J.
Mutations in the central part of a Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after troponin–tropomyosin removal and reconstitution 2015 Beatrice, Scellini; Nicoletta, Piroddi; Claudia, Ferrara; Matyushenko, Alexander; Levitsky, Dmitrii; Corrado, Poggesi; Chiara, Tesi
R4496C RyR2 mutation impairs atrial and ventricular contractility 2016 Ferrantini, Cecilia; Coppini, Raffaele; Scellini, Beatrice; Ferrara, Claudia; Pioner, Josè Manuel; Mazzoni, Luca; Priori, Silvia; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado
The homozygous K280N troponin T mutation alters cross-bridge kinetics and energetics in human HCM 2019 Piroddi, Nicoletta; Witjas-Paalberends, E. Rosalie; Ferrara, Claudia; Ferrantini, Cecilia; Vitale, Giulia; Scellini, Beatrice; Wijnker, Paul J.M.; Sequiera, Vasco; Dooijes, Dennis; dos Remedios, Cristobal; Schlossarek, Saskia; Leung, Man Ching; Messer, Andrew; Ward, Douglas G.; Biggeri, Annibale; Tesi, Chiara; Carrier, Lucie; Redwood, Charles S.; Marston, Steven B.; van der Velden, Jolanda; Poggesi, Corrado
Mostrati risultati da 1 a 20 di 21
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