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Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model 2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
Myocardial dysfunction in hypertrophic cardiomyopathy (HCM): primary effects of sarcomeric protein mutations versus secondary E-C coupling remodeling 2015 Coppini, Raffaele; Ferrantini, Cecilia; Mazzoni, Luca; Pioner, José Manuel; Tosi, Benedetta; Gentile, Francesca; Piroddi, Nicoletta; Scellini, Beatrice; Tardif, Jil; Tesi, Chiara; Mugelli, Alessandro; Cerbai, Elisabetta; Poggesi, Corrado
Myocardial Dysfunction in Hypertrophic Cardiomyopathy: Primary Effects of Sarcomeric Mutations Versus Secondary EC-Coupling Remodelling 2015 Coppini, Raffaele; Ferrantini, Cecilia; Gentile, Francesca; Mazzoni, Luca; Tosi, Benedetta; Pioner, José Manuel; Scellini, Beatrice; Piroddi, Nicoletta; Tardiff, Jil C; Tesi, Chiara; Cerbai, Elisabetta; Poggesi, Corrado
Novel insights on the relationship between T-tubular defects and contractile dysfunction in a mouse model of hypertrophic cardiomyopathy. 2016 Crocini, C; Ferrantini, C; Scardigli, M; Coppini, R; Mazzoni, L; Lazzeri, E; Pioner, Jm; Scellini, B; Guo, A; Song, Ls; Yan, P; Loew, Lm; Tardiff, J; Tesi, C; Vanzi, F; Cerbai, E; Pavone, Fs; Sacconi, L; Poggesi, C.
R4496C RyR2 mutation impairs atrial and ventricular contractility 2016 Ferrantini, Cecilia; Coppini, Raffaele; Scellini, Beatrice; Ferrara, Claudia; Pioner, Josè Manuel; Mazzoni, Luca; Priori, Silvia; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado
Contractile properties of developing human fetal cardiac muscle 2016 Alice W. Racca, Jordan M. Klaiman, Josè Manuel Pioner, Yuanhua Cheng, Anita E. Beck, Farid Moussavi-Harami, Michael J. Bamshad, Michael Regnier
Isolation and Mechanical Measurements of Myofibrils from Human Induced Pluripotent Stem Cell-Derived Cardiomyocytes. 2016 Pioner, Jm; Racca, Aw; Klaiman, Jm; Yang, Kc; Guan, X; Pabon, L; Muskheli, V; Zaunbrecher, R; Macadangdang, J; Jeong, My; Mack, Dl; Childers, Mk; Kim, Dh; Tesi, C; Poggesi, C; Murry, Ce; Regnier, M
Atrial Remodeling in Hypertrophic Cardiomyopathy 2017 Ferrantini, Cecilia; Pioner, Josè Manuel; Gentile, Francesca; Coppini, Raffaele; Morelli, Cristina; Piroddi, Nicoletta; Scellini, Beatrice; Cerbai, Elisabetta; Tardiff, Jil; Tesi, Chiara; Olivotto, Iacopo; Poggesi, Corrado
Liquid Crystalline Networks toward Regenerative Medicine and Tissue Repair 2017 Martella, Daniele; Paoli, Paolo; Pioner, JOSE' MANUEL; Sacconi, Leonardo; Coppini, Raffaele; Santini, Lorenzo; Lulli, Matteo; Cerbai, Elisabetta; Wiersma, DIEDERIK SYBOLT; Poggesi, Corrado; Ferrantini, Cecilia; Parmeggiani, Camilla
Ranolazine prevents phenotype development in a mouse model of hypertrophic cardiomyopathy 2017 Coppini, Raffaele; Mazzoni, Luca; Ferrantini, Cecilia; Gentile, Francesca; Pioner, Josè Manuel; Laurino, Annunziatina; Santini, Lorenzo; Bargelli, Valentina; Rotellini, Matteo; Bartolucci, Gian Luca; Crocini, Claudia; Sacconi, Leonardo; Tesi, Chiara; Belardinelli, Luiz; Tardiff, Jil; Mugelli, Alessandro; Olivotto, Iacopo; Cerbai, Elisabetta; Poggesi, Corrado
Pathogenesis of hypertrophic cardiomyopathy is mutation rather than disease specific: A comparison of the cardiac troponin T E163R and R92Q mouse models 2017 Ferrantini, Cecilia; Coppini, Raffaele; Pioner, JOSE' MANUEL; Gentile, Francesca; Tosi, Benedetta; Mazzoni, Luca; Scellini, Beatrice; Piroddi, Nicoletta; Laurino, Annunziatina; Santini, Lorenzo; Spinelli, Valentina; Sacconi, Leonardo; De Tombe, Pieter; Moore, Rachel; Tardiff, Jil; Mugelli, Alessandro; Olivotto, Iacopo; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado
Design of muscle contraction assist devices by liquid crystalline elastomers 2018 Cecilia Ferrantini , José Manuel Pioner, Daniele Martella, Raffaele Coppini, Nicoletta Piroddi, Francesco Saverio Pavone, Diederik Sybolt Wiersma, Chiara Tesi, Elisabetta Cerbai, Corrado Poggesi, Leonardo Sacconi, Camilla Parmeggiani
The missense E258 K-MyBP-C mutation increases the energy cost of tension generation in both ventricular and atrial tissue from HCM patients 2018 Giulia Vitale, Nicoletta Piroddi, Beatrice Scellini, Josè Manuel Pioner, Cecilia Ferrantini, Chiara Tesi, Corrado Poggesi
The Missense E258K-MyBP-C Mutation Increases the Energy Cost of Tension Generation in Both Ventricular and Atrial Tissue from HCM Patients 2018 Vitale, Giulia; Gentile, Francesca; Piroddi, Nicoletta; Scellini, Beatrice; Pioner, Josè Manuel; Olivotto, Iacopo; Ferrantini, Cecilia; Tesi, Chiara; Poggesi, Corrado
Late sodium current inhibitors to treat exercise induced obstruction in hypertrophic cardiomyopathy: an in vitro study in human myocardium. 2018 Cecilia Ferrantini, Josè Manuel Pioner, Luca Mazzoni, Francesca Gentile, Benedetta Tosi, Alessandra Rossi, Luiz Belardinelli, Chiara Tesi, Chiara Palandri, Rosanna Matucci, Elisabetta Cerbai, Iacopo Olivotto, Corrado Poggesi, Alessandro Mugelli, Raffaele Coppini
Advanced Morpho-Functional Analysis on Ventricular and Atrial Tissue Reveals Cross-Bridge Kinetics Alterations and Sarcomere Energetic Impairment in Hcm Patients 2019 Vitale, G; Lazzeri, E; Costantini, I; Giardini, F; Mazzamuto, G; Crocini, C; Piroddi, N; Scellini, B; Pioner, JM; Ferrantini, C; Tesi, C; Pavone, FS; Sacconi, L; Poggesi, C
Optical investigation of action potential and calcium handling maturation of hiPSC-cardiomyocytes on biomimetic substrates 2019 Pioner J.M.; Santini L.; Palandri C.; Martella D.; Lupi F.; Langione M.; Querceto S.; Grandinetti B.; Balducci V.; Benzoni P.; Landi S.; Barbuti A.; Lupi F.F.; Boarino L.; Sartiani L.; Tesi C.; Mack D.L.; Regnier M.; Cerbai E.; Parmeggiani C.; Poggesi C.; Ferrantini C.; Coppini R.
Design of Biocompatible Liquid Cristal Elastomers Reproducing the Mechanical Properties of Human Cardiac Muscle 2019 Ferrantini, C; Pioner, JM; Martella, D; Coppini, R; Piroddi, N; Paoli, P; Calamai, M; Pavone, FS; Wiersma, D; Tesi, C; Cerbai, E; Poggesi, C; Sacconi, L; Parmeggiani, C
Electrophysiological and Contractile Effects of Disopyramide in Patients With Obstructive Hypertrophic Cardiomyopathy: a Translational Study 2019 Coppini, Raffaele; Ferrantini, Cecilia; Pioner, Josè Manuel; Santini, Lorenzo; Wang, Zhinuo J.; Palandri, Chiara; Scardigli, Marina; Vitale, Giulia; Sacconi, Leonardo; Stefàno, Pierluigi; Flink, Laura; Riedy, Katherine; Pavone, Francesco Saverio; Cerbai, Elisabetta; Poggesi, Corrado; Mugelli, Alessandro; Bueno-Orovio, Alfonso; Olivotto, Iacopo; Sherrid, Mark V.
Absence of full-length dystrophin impairs normal maturation and contraction of cardiomyocytes derived from human induced pluripotent stem cells 2019 Pioner, J. M.; Guan, Xuan; Klaiman, Jordan M; Racca, Alice W; Pabon, Lil; Muskheli, Veronica; Macadangdang, Jesse; Ferrantini, Cecilia; Hoopmann, Michael R; Moritz, Robert L; Kim, Deok-Ho; Tesi, Chiara; Poggesi, Corrado; Murry, Charles E; Childers, Martin K; Mack, David L; Regnier, Michael
Mostrati risultati da 1 a 20 di 37
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