Sporadic Creutzfeldt-Jakob disease (CJD) is a rare neurodegenerative disease caused by prions that is randomly distributed in all countries, with an overall yearly mortality rate of about 1-2 cases per million people. On a few occasions, however, sporadic CJD occurred with higher than expected rates, but further investigations failed to recognize any convincing causal link. In Italy, cluster analyses of sporadic CJD cases have not been performed previously.

Spatial Epidemiology of Sporadic Creutzfeldt-Jakob Disease in Apulia, Italy / Puopolo, Maria; Catelan, Dolores; Capellari, Sabina; Ladogana, Anna; Sanguedolce, Antonio; Fedele, Alberto; Aprile, Valerio; Turco, Giuseppa Lucia; Colaizzo, Elisa; Tiple, Dorina; Vaianella, Luana; Parchi, Piero; Biggeri, Annibale; Pocchiari, Maurizio. - In: NEUROEPIDEMIOLOGY. - ISSN 0251-5350. - ELETTRONICO. - (2019), pp. 1-7-1-7. [10.1159/000503234]

Spatial Epidemiology of Sporadic Creutzfeldt-Jakob Disease in Apulia, Italy

Catelan, Dolores;Biggeri, Annibale;
2019

Abstract

Sporadic Creutzfeldt-Jakob disease (CJD) is a rare neurodegenerative disease caused by prions that is randomly distributed in all countries, with an overall yearly mortality rate of about 1-2 cases per million people. On a few occasions, however, sporadic CJD occurred with higher than expected rates, but further investigations failed to recognize any convincing causal link. In Italy, cluster analyses of sporadic CJD cases have not been performed previously.
2019
1-7
1-7
Puopolo, Maria; Catelan, Dolores; Capellari, Sabina; Ladogana, Anna; Sanguedolce, Antonio; Fedele, Alberto; Aprile, Valerio; Turco, Giuseppa Lucia; Colaizzo, Elisa; Tiple, Dorina; Vaianella, Luana; Parchi, Piero; Biggeri, Annibale; Pocchiari, Maurizio
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Utilizza questo identificatore per citare o creare un link a questa risorsa: https://hdl.handle.net/2158/1172393
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