Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare systemic vasculitis. Cardiac specific involvement (CSI) is caused by coronary artery vasculitis, but also by myocardial eosinophilic infiltration. To date, the prevalence of CSI associated with EGPA is unresolved. Aim of this study was to systematically assess the prevalence and clinical impact of CSI in a consecutive outpatient EGPA population.
Cardiac involvement in eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome): Prospective evaluation at a tertiary referral centre / Zampieri, Mattia; Emmi, Giacomo; Beltrami, Matteo; Fumagalli, Carlo; Urban, Maria Letizia; Dei, Lupo; Marchi, Alberto; Berteotti, Martina; Tomberli, Alessia; Baldini, Katia; Bettiol, Alessandra; Pradella, Silvia; Silvestri, Elena; Marchionni, Niccolò; Vaglio, Augusto; Olivotto, Iacopo; Prisco, Domenico. - In: EUROPEAN JOURNAL OF INTERNAL MEDICINE. - ISSN 1879-0828. - ELETTRONICO. - (2020), pp. 30451-30459. [10.1016/j.ejim.2020.12.008]
Cardiac involvement in eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome): Prospective evaluation at a tertiary referral centre
Zampieri, Mattia;Emmi, Giacomo;Beltrami, Matteo;Fumagalli, Carlo;Urban, Maria Letizia;Dei, Lupo;Marchi, Alberto;Berteotti, Martina;Tomberli, Alessia;Bettiol, Alessandra;Pradella, Silvia;Silvestri, Elena;Marchionni, Niccolò;Vaglio, Augusto;Olivotto, Iacopo;Prisco, Domenico
2020
Abstract
Eosinophilic granulomatosis with polyangiitis (EGPA) is a rare systemic vasculitis. Cardiac specific involvement (CSI) is caused by coronary artery vasculitis, but also by myocardial eosinophilic infiltration. To date, the prevalence of CSI associated with EGPA is unresolved. Aim of this study was to systematically assess the prevalence and clinical impact of CSI in a consecutive outpatient EGPA population.| File | Dimensione | Formato | |
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