Introduction: Variants in the desmoplakin (DSP) gene are associated with a form of arrhythmogenic cardiomyopathy (ACM) characterized by high risk of ventricular arrhythmias (VAs), heart failure (HF), and recurrent myocarditis. The clinical implications and management of myocarditis episodes in DSP-ACM have been scarcely investigated and are a major unmet clinical challenge.

Abstract 4142400: Clinical implication and potential role of immunosuppression for myocarditis episodes in patients with desmoplakin cardiomyopathy: hope from the DSP-ERADOS Network? / Gasperetti, A., Peretto, G., Muller, S., Laredo, m., Carrick, R., Asatryan, B., Protonotarios, A., Murray, B., Scheel, P., Pilichou, K., Syrris, P., Jason, M., Medo, K., Rossi, V., Saguner, A., Hylind, R., Abrams, D., Cadrin-Tourigny, J., olivotto, i., Biagini, E., et al.. - In: CIRCULATION. - ISSN 0009-7322. - ELETTRONICO. - 150:(2024), pp. 0-0. [10.1161/circ.150.suppl_1.4142400]

Abstract 4142400: Clinical implication and potential role of immunosuppression for myocarditis episodes in patients with desmoplakin cardiomyopathy: hope from the DSP-ERADOS Network?

olivotto, iacopo;Mestroni, Luisa;Sinagra, Gianfranco;
2024

Abstract

Introduction: Variants in the desmoplakin (DSP) gene are associated with a form of arrhythmogenic cardiomyopathy (ACM) characterized by high risk of ventricular arrhythmias (VAs), heart failure (HF), and recurrent myocarditis. The clinical implications and management of myocarditis episodes in DSP-ACM have been scarcely investigated and are a major unmet clinical challenge.
2024
Gasperetti, Alessio; Peretto, Giovanni; Muller, Steven; Laredo, mikael; Carrick, Richard; Asatryan, Babken; Protonotarios, Alexandros; Murray, Brittne...espandi
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Utilizza questo identificatore per citare o creare un link a questa risorsa: https://hdl.handle.net/2158/1402063
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