Kikuchi-Fujimoto disease (KFD) is a rare and benign lymphadenopathy of unknown etiology. Usually, it is an isolated and self-limiting condition requiring no specific therapy; however, in some cases, it may be associated with an autoimmune disease. Here, we report three cases of KFD developing an associated autoimmune connective disorder: the first case presented with Sjögren’s syndrome, and the other two had a diagnosis of systemic lupus erythematosus.
Rare in the rare: Kikuchi-Fujimoto disease associated with connective tissue disorders. A report of our experience / Coccia, Carmela; Lepri, Gemma; Levani, Juela; Bellando Randone, Silvia; Guiducci, Serena. - In: REUMATISMO. - ISSN 0048-7449. - ELETTRONICO. - 77:(2025), pp. 1853.0-1853.0. [10.4081/reumatismo.2025.1853]
Rare in the rare: Kikuchi-Fujimoto disease associated with connective tissue disorders. A report of our experience
Coccia, Carmela;Lepri, Gemma;Levani, Juela;Bellando Randone, Silvia;Guiducci, Serena
2025
Abstract
Kikuchi-Fujimoto disease (KFD) is a rare and benign lymphadenopathy of unknown etiology. Usually, it is an isolated and self-limiting condition requiring no specific therapy; however, in some cases, it may be associated with an autoimmune disease. Here, we report three cases of KFD developing an associated autoimmune connective disorder: the first case presented with Sjögren’s syndrome, and the other two had a diagnosis of systemic lupus erythematosus.I documenti in FLORE sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.



