To asses the characteristics of severe action myoclonus in three patients with progressive myoclonus epilepsy (PME) due to sialidosis. We assessed EEG-EMG coherence, relative power (RP) and bandwidth (BW) of the EMG-peak associated with myoclonus; we also evaluated somatosensory evoked potentials and long-loop reflexes (LLRs). We compared the findings with those obtained in ten Unverricht-Lundborg (UL) patients.
Characterization of severe action myoclonus in sialidoses / Canafoglia L; Franceschetti S; Uziel G; Ciano C; Scaioli V; Guerrini R; Visani E; Panzica F.. - In: EPILEPSY RESEARCH. - ISSN 0920-1211. - STAMPA. - 94 (1-2):(2011), pp. 86-93. [10.1016/j.eplepsyres.2011.01.013]
Characterization of severe action myoclonus in sialidoses.
GUERRINI, RENZO;
2011
Abstract
To asses the characteristics of severe action myoclonus in three patients with progressive myoclonus epilepsy (PME) due to sialidosis. We assessed EEG-EMG coherence, relative power (RP) and bandwidth (BW) of the EMG-peak associated with myoclonus; we also evaluated somatosensory evoked potentials and long-loop reflexes (LLRs). We compared the findings with those obtained in ten Unverricht-Lundborg (UL) patients.I documenti in FLORE sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.