| Nome |
# |
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Mavacamten for treatment of symptomatic obstructive hypertrophic cardiomyopathy (EXPLORER-HCM): a randomised, double-blind, placebo-controlled, phase 3 trial, file e398c37f-e933-179a-e053-3705fe0a4cff
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4.318
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Role of genetic testing in inherited cardiovascular disease: A review, file e398c37f-5145-179a-e053-3705fe0a4cff
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931
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Pharmacological treatment of hypertrophic cardiomyopathy: current practice and novel perspectives, file e398c37f-4965-179a-e053-3705fe0a4cff
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516
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Unmasking the prevalence of amyloid cardiomyopathy in the real world: results from Phase 2 of the AC-TIVE study, an Italian nationwide survey, file eeb5b737-82d4-4001-b54f-bd07ceac5fac
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381
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Microvascular dysfunction, myocardial ischemia, and progression to heart failure in patients with hypertrophic cardiomyopathy, file e398c37e-167c-179a-e053-3705fe0a4cff
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370
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Significance of Late Gadolinium Enhancement at Right Ventricular Attachment to Ventricular Septum in Patients with Hypertrophic Cardiomyopathy, file e398c37f-25c4-179a-e053-3705fe0a4cff
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336
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The coronary circulation and blood flow in left ventricular hypertrophy, file e398c37f-4aad-179a-e053-3705fe0a4cff
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328
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Multidisciplinary evaluation and management of obstructive hypertrophic cardiomyopathy in 2020: Towards the HCM Heart Team, file e398c37f-d67a-179a-e053-3705fe0a4cff
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302
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Participation in thrill-seeking activities by patients with hypertrophic cardiomyopathy: Individual preferences, adverse events and physician attitude, file e398c37f-3fd5-179a-e053-3705fe0a4cff
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286
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Sex-related differences in exercise performance and outcome of patients with hypertrophic cardiomyopathy, file e398c37f-085f-179a-e053-3705fe0a4cff
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249
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|
Microvascular function is selectively impaired in patients with hypertrophic cardiomyopathy and sarcomere myofilament gene mutations., file e398c378-c0ef-179a-e053-3705fe0a4cff
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245
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Spectrum and clinical significance of systolic function and myocardial fibrosis assessed by cardiovascular magnetic resonance in hypertrophic cardiomyopathy, file e398c37e-819e-179a-e053-3705fe0a4cff
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241
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Intraoperative diagnosis of Anderson-Fabry disease in patients with obstructive hypertrophic cardiomyopathy undergoing surgical myectomy, file e398c37f-0861-179a-e053-3705fe0a4cff
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239
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β Blockers for prevention of exercise-induced left ventricular outflow tract obstruction in patients with hypertrophic cardiomyopathy, file e398c37d-4ac4-179a-e053-3705fe0a4cff
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234
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An Investigation of the Molecular Mechanism of Double cMyBP-C Mutation in a Patient with End-Stage Hypertrophic Cardiomyopathy, file e398c37e-f5d9-179a-e053-3705fe0a4cff
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227
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Relationship between atrial fibrillation and blunted hyperemic myocardial blood flow in patients with hypertrophic cardiomyopathy., file e398c378-ab26-179a-e053-3705fe0a4cff
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225
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Cardioprotective Strategy for Patients with Nonmetastatic Breast Cancer Who Are Receiving an Anthracycline-Based Chemotherapy: A Randomized Clinical Trial, file e398c381-a002-179a-e053-3705fe0a4cff
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215
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Comparison of long-term outcome in anthracycline-related versus idiopathic dilated cardiomyopathy: a single centre experience, file e398c37d-4d83-179a-e053-3705fe0a4cff
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211
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Mavacamten for hypertrophic obstructive cardiomyopathy – Authors' reply, file e398c382-04a5-179a-e053-3705fe0a4cff
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195
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Role of cardiovascular magnetic resonance in the clinical evaluation of left ventricular hypertrophy: a 360° panorama, file 4b71c1ef-cf6a-4781-963c-e8ad94dd4850
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176
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Spatial and Functional Distribution of MYBPC3 Pathogenic Variants and Clinical Outcomes in Patients with Hypertrophic Cardiomyopathy, file e398c37f-f2e9-179a-e053-3705fe0a4cff
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166
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Usefulness of Electrocardiographic Patterns at Presentation to Predict Long-term Risk of Cardiac Death in Patients With Hypertrophic Cardiomyopathy, file e398c37e-f396-179a-e053-3705fe0a4cff
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165
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Late sodium current inhibitors to treat exercise induced obstruction in hypertrophic cardiomyopathy: an in vitro study in human myocardium., file e398c37d-346f-179a-e053-3705fe0a4cff
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163
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Clinical Features and Outcome of Hypertrophic Cardiomyopathy Associated With Triple Sarcomere Protein Gene Mutations, file e398c37e-7d5f-179a-e053-3705fe0a4cff
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162
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Changes in the perceived epidemiology of amyloidosis: 20 year-experience from a Tertiary Referral Centre in Tuscany, file e398c381-c99e-179a-e053-3705fe0a4cff
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162
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Clinical Course and Significance of Hypertrophic Cardiomyopathy Without Left Ventricular Hypertrophy, file e398c37e-ef27-179a-e053-3705fe0a4cff
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153
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Pathogenesis of hypertrophic cardiomyopathy is mutation rather than disease specific: A comparison of the cardiac troponin T E163R and R92Q mouse models, file e398c37d-1602-179a-e053-3705fe0a4cff
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152
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Can anthropology improve our care of inherited cardiac arrhythmias? A modest proposal, file e398c37f-4ea2-179a-e053-3705fe0a4cff
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151
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|
Validation of pixel-wise parametric mapping of myocardial blood flow with ¹³NH₃ PET in patients with hypertrophic cardiomyopathy., file e398c379-d580-179a-e053-3705fe0a4cff
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141
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|
Atrial Remodeling in Hypertrophic Cardiomyopathy, file e398c37c-6469-179a-e053-3705fe0a4cff
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141
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The familial hypertrophic cardiomyopathy-associated myosin mutation R403Q accelerates tension generation and relaxation of human cardiac myofibrils, file e398c37d-52b3-179a-e053-3705fe0a4cff
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140
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|
Advances in Stem Cell Modeling of Dystrophin-Associated Disease: Implications for the Wider World of Dilated Cardiomyopathy, file e398c37f-be3f-179a-e053-3705fe0a4cff
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140
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Incremental prognostic value of multiparametric echocardiographic assessment for severe aortic stenosis, file e398c37e-fa3c-179a-e053-3705fe0a4cff
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136
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Obesity and its association to phenotype and clinical course in hypertrophic cardiomyopathy, file e398c37e-c215-179a-e053-3705fe0a4cff
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134
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Timing and significance of exercise-induced left ventricular outflow tract pressure gradients in hypertrophic cardiomyopathy, file e398c37e-e6f2-179a-e053-3705fe0a4cff
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132
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Oral pharmacological chaperone migalastat compared with enzyme replacement therapy in Fabry disease: 18-month results from the randomised phase III ATTRACT study, file e398c37f-4bf8-179a-e053-3705fe0a4cff
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132
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Novel Approach Targeting the Complex Pathophysiology of Hypertrophic Cardiomyopathy: The Impact of Late Sodium Current Inhibition on Exercise Capacity in Subjects with Symptomatic Hypertrophic Cardiomyopathy (LIBERTY-HCM) Trial, file e398c37f-4ea4-179a-e053-3705fe0a4cff
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121
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Echocardiography in patients with hypertrophic cardiomyopathy: Usefulness of old and new techniques in the diagnosis and pathophysiological assessment, file e398c37e-d7e3-179a-e053-3705fe0a4cff
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119
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Regulation of intracellular Na+ in health and disease: pathophysiological mechanisms and implications for treatment, file e398c378-ee55-179a-e053-3705fe0a4cff
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117
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Myocardial bridging and sudden death in hypertrophic cardiomyopathy: Salome drops another veil, file e398c37e-e8a5-179a-e053-3705fe0a4cff
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117
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Microvascular ischaemia after cardiac arrest in a patient with hypertrophic cardiomyopathy, file e398c37f-25c6-179a-e053-3705fe0a4cff
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116
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Electrophysiological and Contractile Effects of Disopyramide in Patients With Obstructive Hypertrophic Cardiomyopathy: a Translational Study, file e398c37e-b9c1-179a-e053-3705fe0a4cff
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114
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Study Design and Rationale of EXPLORER-HCM: Evaluation of Mavacamten in Adults with Symptomatic Obstructive Hypertrophic Cardiomyopathy, file e398c37f-f27b-179a-e053-3705fe0a4cff
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108
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Reevaluating the Genetic Contribution of Monogenic Dilated Cardiomyopathy, file e398c380-53ea-179a-e053-3705fe0a4cff
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107
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Multidimensional structure-function relationships in human β-cardiac myosin from population-scale genetic variation, file e398c37f-0dad-179a-e053-3705fe0a4cff
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106
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Contemporary Insights Into the Genetics of Hypertrophic Cardiomyopathy: Toward a New Era in Clinical Testing?, file e398c37f-6180-179a-e053-3705fe0a4cff
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105
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"Tuscany Registry for sAdden Cardiac DEath": metodo per la creazione di un registro multicentrico per la gestione di eventi di morte improvvisa in età giovanile, file e398c37d-5b52-179a-e053-3705fe0a4cff
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103
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Hemodynamic progression and outcome of asymptomatic aortic stenosis in primary care, file e398c37e-a114-179a-e053-3705fe0a4cff
|
102
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Impact of demographic features, lifestyle, and comorbidities on the clinical expression of hypertrophic cardiomyopathy, file e398c37f-06f3-179a-e053-3705fe0a4cff
|
102
|
|
Electromechanical dissociation of left atrium in patients with Cardiac Amyloidosis by Magnetic Resonance: Prognostic and clinical correlates, file e398c37f-e43a-179a-e053-3705fe0a4cff
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102
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The Portuguese Registry of Hypertrophic Cardiomyopathy: Overall results, file e398c37e-f161-179a-e053-3705fe0a4cff
|
100
|
|
Heritability in genetic heart disease: The role of genetic background, file e398c37e-a556-179a-e053-3705fe0a4cff
|
96
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Life-Threatening Acute Pulmonary Thromboembolism Following Severe Carbon Monoxide Poisoning, file e398c37f-1215-179a-e053-3705fe0a4cff
|
96
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International external validation study of the 2014 European society of cardiology guidelines on sudden cardiac death prevention in hypertrophic cardiomyopathy (EVIDENCE-HCM), file e398c37f-288f-179a-e053-3705fe0a4cff
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94
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Slower Calcium Handling Balances Faster Cross-Bridge Cycling in Human MYBPC3 HCM, file 64fa5412-d167-40bd-a0da-09e84b46c566
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93
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Dissecting functional impairment in hypertrophic cardiomyopathy by dynamic assessment of diastolic reserve and outflow obstruction: A combined cardiopulmonary-echocardiographic study, file e398c37f-25c2-179a-e053-3705fe0a4cff
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91
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Acceptability, Feasibility and Preliminary Evaluation of a Novel, Personalised, Home-Based Physical Activity Intervention for Chronic Heart Failure (Active-at-Home-HF): a Pilot Study, file e398c37f-4e34-179a-e053-3705fe0a4cff
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91
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The Importance of Sex Differences in Patients with Hypertrophic Cardiomyopathy – Tailoring Management and Future Perspectives, file e398c37f-fc62-179a-e053-3705fe0a4cff
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90
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Effect of Mavacamten on Echocardiographic Features in Symptomatic Patients With Obstructive Hypertrophic Cardiomyopathy, file e398c381-998f-179a-e053-3705fe0a4cff
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88
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Cardiac Involvement in Fabry Disease: JACC Review Topic of the Week, file b1c1f4dd-1301-4c85-8de1-e8a221b957d6
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87
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The Missense E258K-MyBP-C Mutation Increases the Energy Cost of Tension Generation in Both Ventricular and Atrial Tissue from HCM Patients, file e398c37e-be0c-179a-e053-3705fe0a4cff
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87
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Clinical profile and outcome of cardiac involvement in MELAS syndrome, file e398c37f-25ea-179a-e053-3705fe0a4cff
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87
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A Validated Model for Sudden Cardiac Death Risk Prediction in Pediatric Hypertrophic Cardiomyopathy, file e398c37f-617e-179a-e053-3705fe0a4cff
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85
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|
Prevalence and clinical significance of acquired left coronary artery fistulas after surgical myectomy in patients with hypertrophic cardiomyopathy, file e398c37e-8369-179a-e053-3705fe0a4cff
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84
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Quantitative approaches to variant classification increase the yield and precision of genetic testing in Mendelian diseases: The case of hypertrophic cardiomyopathy, file e398c37e-bb0f-179a-e053-3705fe0a4cff
|
83
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Contemporary genetic testing in inherited cardiac disease: Tools, ethical issues, and clinical applications, file e398c37f-15ba-179a-e053-3705fe0a4cff
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82
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Significance of sarcomere gene mutations analysis in the end-stage phase of hypertrophic cardiomyopathy, file e398c37f-4778-179a-e053-3705fe0a4cff
|
78
|
|
Left Ventricular Apex Involvement in Hypertrophic Cardiomyopathy, file e398c37f-2f70-179a-e053-3705fe0a4cff
|
76
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|
Reversible dilated cardiomyopathy: into the thaumaturgy of the heart - Part 2, file e398c37e-ef9c-179a-e053-3705fe0a4cff
|
75
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|
Stress echo 2020: The international stress echo study in ischemic and non-ischemic heart disease, file e398c37f-0daf-179a-e053-3705fe0a4cff
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75
|
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Molecular Modeling of Disease Causing Mutations in Domain C1 of cMyBP-C, file e398c37f-5464-179a-e053-3705fe0a4cff
|
75
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Care in Specialized Centers and Data Sharing Increase Agreement in Hypertrophic Cardiomyopathy Genetic Test Interpretation, file e398c37f-15b3-179a-e053-3705fe0a4cff
|
74
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On the Cardiac Loop and Its Failing: Left Ventricular Outflow Tract Obstruction, file e398c37f-9b35-179a-e053-3705fe0a4cff
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74
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|
MR imaging in hypertrophic cardiomyopathy: From magnet to bedside, file e398c37e-adaa-179a-e053-3705fe0a4cff
|
71
|
|
Effects of myocardial fibrosis assessed by MRI on dynamic left ventricular outflow tract obstruction in patients with hypertrophic cardiomyopathy: A retrospective database analysis, file e398c37f-567b-179a-e053-3705fe0a4cff
|
71
|
|
Sex-related differences in clinical presentation and all-cause mortality in patients with cardiac transthyretin amyloidosis and light chain amyloidosis, file e398c381-fcc5-179a-e053-3705fe0a4cff
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71
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|
Temporal Trend of Age at Diagnosis in Hypertrophic Cardiomyopathy: An Analysis of the International Sarcomeric Human Cardiomyopathy Registry, file e398c37f-d3b9-179a-e053-3705fe0a4cff
|
70
|
|
Clinical Features and Natural History of PRKAG2 Variant Cardiac Glycogenosis, file e398c380-4319-179a-e053-3705fe0a4cff
|
70
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IN VIVO OBSERVATION OF RETINAL VASCULAR DEPOSITS USING ADAPTIVE OPTICS IMAGING IN FABRY DISEASE, file e398c37f-37dc-179a-e053-3705fe0a4cff
|
67
|
|
Transcatheter ablation for atrial fibrillation in patients with hypertrophic cardiomyopathy: Long-term results and clinical outcomes, file e398c381-f2cc-179a-e053-3705fe0a4cff
|
67
|
|
The electrocardiogram in the diagnosis and management of patients with dilated cardiomyopathy, file e398c37f-a760-179a-e053-3705fe0a4cff
|
64
|
|
Cardiac Resynchronization Therapy for End-Stage Hypertrophic Cardiomyopathy: The Need for Disease-Specific Criteria, file e398c37e-e4dc-179a-e053-3705fe0a4cff
|
63
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|
Life-long tailoring of management for patients with hypertrophic cardiomyopathy: Awareness and decision-making in changing scenarios, file e398c37f-5143-179a-e053-3705fe0a4cff
|
63
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|
Myosin Sequestration Regulates Sarcomere Function, Cardiomyocyte Energetics, and Metabolism, Informing the Pathogenesis of Hypertrophic Cardiomyopathy, file e398c37f-6193-179a-e053-3705fe0a4cff
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61
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|
Predictors of mortality and adverse events in patients with infective endocarditis: a retrospective real world study in a surgical centre, file e398c380-9495-179a-e053-3705fe0a4cff
|
61
|
|
Doctor-patient care relationship in genetic cardiomyopathies: An exploratory study on clinical consultations, file e398c37f-d753-179a-e053-3705fe0a4cff
|
60
|
|
Defining the diagnostic effectiveness of genes for inclusion in panels: the experience of two decades of genetic testing for hypertrophic cardiomyopathy at a single center, file e398c380-6b4e-179a-e053-3705fe0a4cff
|
60
|
|
Genetic characterization of juvenile sudden cardiac arrest and death in Tuscany: The ToRSADE registry, file 65cf5939-4f21-40c7-a334-075620af6ca7
|
59
|
|
Genotype and lifetime burden of disease in hypertrophic cardiomyopathy insights from the sarcomeric human cardiomyopathy registry (SHaRe), file e398c37e-f164-179a-e053-3705fe0a4cff
|
59
|
|
Impact of cardiovascular involvement on the clinical course of paediatric mitochondrial disorders, file e398c37f-d7ca-179a-e053-3705fe0a4cff
|
59
|
|
Genetic determinants of clinical phenotype in hypertrophic cardiomyopathy, file e398c380-8fdf-179a-e053-3705fe0a4cff
|
59
|
|
Cardiogenic Shock in Obstructive Hypertrophic Cardiomyopathy Plus Apical Ballooning: Management With VA-ECMO and Myectomy, file e398c380-ea8b-179a-e053-3705fe0a4cff
|
59
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|
Design of the SILICOFCM study: Effect of sacubitril/valsartan vs lifestyle intervention on functional capacity in patients with hypertrophic cardiomyopathy, file e398c37f-89f1-179a-e053-3705fe0a4cff
|
58
|
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Comprehensive Risk Management in Arrhythmogenic Cardiomyopathy Associated With Autosomal Dominant Carvajal Syndrome, file e398c37f-d7cc-179a-e053-3705fe0a4cff
|
58
|
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Mitochondrial Energetics and Ca2+-Activated ATPase in Obstructive Hypertrophic Cardiomyopathy, file e398c380-23da-179a-e053-3705fe0a4cff
|
57
|
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Beta-Blockers for Prevention of Exercise-induced Left Ventricular Outflow Obstruction in Patients with Hypertrophic Cardiomyopathy, file e398c37e-ae96-179a-e053-3705fe0a4cff
|
56
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|
Sex related differences in exercise performance in patients with hypertrophic cardiomyopathy: hemodynamic insights through non-invasive pressure volume analysis, file e398c381-be83-179a-e053-3705fe0a4cff
|
56
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Prevalence of anxiety and depression symptoms in a sample of outpatients with ATTR cardiac amyloidosis, file 3dc09e37-e4ce-4bc8-beb1-57dc7a28c8f8
|
54
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Hypertrophic Cardiomyopathy With Left Ventricular Systolic Dysfunction: Insights From the SHaRe Registry, file e398c37f-9b39-179a-e053-3705fe0a4cff
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54
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Feasibility of a combined mobile-health electrocardiographic and rapid diagnostic test screening for chagas-related cardiac alterations, file e398c381-a2a2-179a-e053-3705fe0a4cff
|
53
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| Totale |
17.755 |