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Titolo Data di pubblicazione Autore(i) File
Impact of R4496C RyR2 mutation on myocardial contractility 2011 Raffaele Coppini; Cecilia Ferrantini; Claudia Ferrara; Beatrice Scellini; Francesca Stillitano; Chiara Tesi; Elisabetta Cerbai; Silvia Priori; Corrado Poggesi
The HCM-Associated Cardiac Troponin T Mutation K273N Accelerates Tension Generation and Relaxation in Human Cardiac Myofibrils 2011 Claudia Ferrara; Nicoletta Piroddi; Beatrice Scellini; Cecilia Ferrantini; Sabine J. van Dijk; Cris dos Remedios; Chiara Tesi; Jolanda van der Velden; Corrado Poggesi
Role of tropomyosin (Tm) isoforms in skeletal muscle thin filament regulation 2011 Scellini B.; Lundy S.; Piroddi N.; Flint G.; Tu A.; Luo Z.; Gordon AM; Regnier M.; Poggesi C.; Tesi C
Age-related decline in contractile function of ventricular myofibrils from HCM patients carrying MYBPC3 mutations 2011 Ferrantini C.; Belus A.; Piroddi N.; Ferrara C.; Scellini B.; Tesi C.; Cecchi F.; Olivotto I.; Poggesi C.
Novel method of obtaining myofibrils from cardiomyocyte cultures 2012 Jeong M.; Ferrara C.; Ferrantini C.; Coppini R.; Scellini B.; Piroddi N.; Tesi C.; Cerbai E.; Poggesi C.
The HCM-associated cardiac Troponin T mutation K280N accelerates tension generation and relaxation in human cardiac myofibrils 2012 Ferrara C; Piroddi N; Scellini B; Ferrantini C; Sequiera V; Remedios C; Carrier L; Tesi C ; Van Der Velden J; Poggesi C.
Tropomyosin D137L of reduced flexibility increases submaximal calcium-activated tension in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution 2012 Beatrice Scellini; Claudia Ferrara; Nicoletta Piroddi; John Sumida; Corrado Poggesi; Sherwin S. Lehrer; Chiara Tesi
Tropomyosin flexibility modulates Ca2+ sensitivity of thin filament and affects tension relaxation in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution 2012 Scellini B.; Ferrara C.; Piroddi N.; Sumida J.; Poggesi C.; Lehrer S.S.; Tesi C.
α-Tropomyosin with a D175N or E180G Mutation in Only One Chain Differs from Tropomyosin with Mutations in Both Chains. 2012 Janco M; Kalyva A; Scellini B; Piroddi N; Tesi C; Poggesi C; Geeves MA.
Increased tension cost in human familial hypertrophic cardiomyopathy caused by the MYH7 mutation R403Q 2013 Witjas-Paalberends R.; Piroddi N.; Scellini B.; Stienen G.; Tesi C.; Poggesi C.; van der Velden J.
The HCM-associated cardiac Troponin T mutation K280N increases the energetic cost of tension generation in human cardiac myofibrils 2013 Ferrara C.; Witjas-Paalberends R.; Piroddi N.; Scellini B.; Tesi C.; Sequiera V.; dos Remedios C.; Schlossarek S.; Leung J; Carrier L.; Redwood C.; Marston S.; van der Velden J.; Poggesi C.
Mutations in MYH7 reduce the force generating capacity of sarcomeres in human familial hypertrophic cardiomyopathy. 2013 Witjas-Paalberends ER; Piroddi N; Stam K; van Dijk SJ; Oliviera VS; Ferrara C; Scellini B; Hazebroek M; Ten Cate FJ; van Slegtenhorst M; Dos Remedios C; Niessen HW; Tesi C; Stienen GJ; Heymans S; Michels M; Poggesi C; van der Velden J.
Tropomyosin Ser-283 pseudo-phosphorylation slows myofibril relaxation. 2013 Nixon BR; Liu B; Scellini B; Tesi C; Piroddi N; Ogut O; John Solaro R; Ziolo MT; Janssen PM; Davis JP; Poggesi C; Biesiadecki BJ.
Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q Myh7 Mutation 2014 Witjas-Paalberends R.; Ferrara C.; Scellini B.; Montag J.; Stienen G.; Kraft T.; Michels M.; Ho C.; Poggesi C.; van der Velden J.
Faster cross-bridge detachment and increased tension cost in human hypertrophic cardiomyopathy with the R403Q MYH7 mutation 2014 Witjas-Paalberends ER; Ferrara C; Scellini B; Piroddi N; Montag J; Tesi C; Stienen GJ; Michels M; Ho CY; Kraft T; Poggesi C; van der Velden J.
Mutations in the central part of α Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after Troponin-Tropomyosin removal and reconstitution 2014 Scellini B
HDAC6 contributes to pathological responses of heart and skeletal muscle to chronic angiotensin-II signaling. 2014 Demos-Davies KM; Ferguson BS; Cavasin MA; Mahaffey JH; Williams SM; Spiltoir JI; Schuetze KB; Horn TR; Chen B; Ferrara C; Scellini B; Piroddi N; Tesi C; Poggesi C; Jeong MY; McKinsey TA
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model 2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
Mutations in the central part of a Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after troponin–tropomyosin removal and reconstitution 2015 Beatrice, Scellini; Nicoletta, Piroddi; Claudia, Ferrara; Matyushenko, Alexander; Levitsky, Dmitrii; Corrado, Poggesi; Chiara, Tesi
Myocardial Dysfunction in Hypertrophic Cardiomyopathy: Primary Effects of Sarcomeric Mutations Versus Secondary EC-Coupling Remodelling 2015 Coppini, Raffaele; Ferrantini, Cecilia; Gentile, Francesca; Mazzoni, Luca; Tosi, Benedetta; Pioner, José Manuel; Scellini, Beatrice; Piroddi, Nicoletta; Tardiff, Jil C; Tesi, Chiara; Cerbai, Elisabetta; Poggesi, Corrado
Mostrati risultati da 21 a 40 di 69
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