FERRARA, CLAUDIA

FERRARA, CLAUDIA  

Medicina Sperimentale e Clinica  

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Titolo Data di pubblicazione Autore(i) File
A Novel Method of Isolating Myofibrils From Primary Cardiomyocyte Culture Suitable for Myofibril Mechanical Study 2019 Woulfe, Kathleen C; Ferrara, Claudia; Pioner, Jose Manuel; Mahaffey, Jennifer H; Coppini, Raffaele; Scellini, Beatrice; Ferrantini, Cecilia; Piroddi, Nicoletta; Tesi, Chiara; Poggesi, Corrado; Jeong, Mark
Age-related decline in contractile function of ventricular myofibrils from HCM patients carrying MYBPC3 mutations 2011 Ferrantini C.; Belus A.; Piroddi N.; Ferrara C.; Scellini B.; Tesi C.; Cecchi F.; Olivotto I.; Poggesi C.
Altered Cross Bridge Kinetics in Skeletal Myofibrils from NEBDex55, a Novel Mouse Model of Nebulin-Based Nemaline Myopathy 2013 Ferrara, Claudia; Buck, Danielle; Piroddi, Nicoletta; Tesi, Chiara; LeWinter, Josine; Ottenheijm, Coen; Poggesi, Corrado; Granzier, Henk
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy 2013 Ottenheijm CA; Buck D; de Winter JM; Ferrara C; Piroddi N; Tesi C; Jasper JR; Malik FI; Meng H; Stienen GJ; Beggs AH; Labeit S; Poggesi C; Lawlor MW; Granzier H
Deleting exon 55 from the nebulin gene induces severe muscle weakness in a mouse model for nemaline myopathy 2013 Ottenheijm, Cac; Buck, D; de Winter, J; Ferrara, Claudia; Piroddi, Nicoletta; Tesi, Chiara; Jasper, R; Malik, F; Meng, F; Stienen, G; Beggs, Ah; Labeit, S; Poggesi, Corrado; Lawlor, M; Granzier, H.
Faster cross-bridge detachment and increased tension cost in human hypertrophic cardiomyopathy with the R403Q MYH7 mutation 2014 Witjas-Paalberends ER; Ferrara C; Scellini B; Piroddi N; Montag J; Tesi C; Stienen GJ; Michels M; Ho CY; Kraft T; Poggesi C; van der Velden J.
Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q Myh7 Mutation 2014 Witjas-Paalberends R.; Ferrara C.; Scellini B.; Montag J.; Stienen G.; Kraft T.; Michels M.; Ho C.; Poggesi C.; van der Velden J.
HDAC6 contributes to pathological responses of heart and skeletal muscle to chronic angiotensin-II signaling. 2014 Demos-Davies KM; Ferguson BS; Cavasin MA; Mahaffey JH; Williams SM; Spiltoir JI; Schuetze KB; Horn TR; Chen B; Ferrara C; Scellini B; Piroddi N; Tesi C; Poggesi C; Jeong MY; McKinsey TA
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model 2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
Impact of R4496C RyR2 mutation on myocardial contractility 2011 Raffaele Coppini; Cecilia Ferrantini; Claudia Ferrara; Beatrice Scellini; Francesca Stillitano; Chiara Tesi; Elisabetta Cerbai; Silvia Priori; Corrado Poggesi
Impact of sarcomeric protein mutations associated to myopathies on the mechanics and energetics of myofibril contraction 2013 Claudia Ferrara
Mutations in MYH7 reduce the force generating capacity of sarcomeres in human familial hypertrophic cardiomyopathy. 2013 Witjas-Paalberends ER; Piroddi N; Stam K; van Dijk SJ; Oliviera VS; Ferrara C; Scellini B; Hazebroek M; Ten Cate FJ; van Slegtenhorst M; Dos Remedios C; Niessen HW; Tesi C; Stienen GJ; Heymans S; Michels M; Poggesi C; van der Velden J.
Mutations in the central part of a Tropomyosin molecule alter Ca2+ sensitivity and tension relaxation of skeletal muscle myofibrils after troponin–tropomyosin removal and reconstitution 2015 Beatrice, Scellini; Nicoletta, Piroddi; Claudia, Ferrara; Matyushenko, Alexander; Levitsky, Dmitrii; Corrado, Poggesi; Chiara, Tesi
Novel method of obtaining myofibrils from cardiomyocyte cultures 2012 Jeong M.; Ferrara C.; Ferrantini C.; Coppini R.; Scellini B.; Piroddi N.; Tesi C.; Cerbai E.; Poggesi C.
R4496C RyR2 mutation impairs atrial and ventricular contractility 2016 Ferrantini, Cecilia; Coppini, Raffaele; Scellini, Beatrice; Ferrara, Claudia; Pioner, Josè Manuel; Mazzoni, Luca; Priori, Silvia; Cerbai, Elisabetta; Tesi, Chiara; Poggesi, Corrado
The HCM-Associated Cardiac Troponin T Mutation K273N Accelerates Tension Generation and Relaxation in Human Cardiac Myofibrils 2011 Claudia Ferrara; Nicoletta Piroddi; Beatrice Scellini; Cecilia Ferrantini; Sabine J. van Dijk; Cris dos Remedios; Chiara Tesi; Jolanda van der Velden; Corrado Poggesi
The HCM-associated cardiac Troponin T mutation K280N accelerates tension generation and relaxation in human cardiac myofibrils 2012 Ferrara C; Piroddi N; Scellini B; Ferrantini C; Sequiera V; Remedios C; Carrier L; Tesi C ; Van Der Velden J; Poggesi C.
The HCM-associated cardiac Troponin T mutation K280N increases the energetic cost of tension generation in human cardiac myofibrils 2013 Ferrara C.; Witjas-Paalberends R.; Piroddi N.; Scellini B.; Tesi C.; Sequiera V.; dos Remedios C.; Schlossarek S.; Leung J; Carrier L.; Redwood C.; Marston S.; van der Velden J.; Poggesi C.
The homozygous K280N troponin T mutation alters cross-bridge kinetics and energetics in human HCM 2019 Piroddi, Nicoletta; Witjas-Paalberends, E. Rosalie; Ferrara, Claudia; Ferrantini, Cecilia; Vitale, Giulia; Scellini, Beatrice; Wijnker, Paul J.M.; Sequiera, Vasco; Dooijes, Dennis; dos Remedios, Cristobal; Schlossarek, Saskia; Leung, Man Ching; Messer, Andrew; Ward, Douglas G.; Biggeri, Annibale; Tesi, Chiara; Carrier, Lucie; Redwood, Charles S.; Marston, Steven B.; van der Velden, Jolanda; Poggesi, Corrado
Tropomyosin D137L of reduced flexibility increases submaximal calcium-activated tension in skeletal muscle myofibrils after troponin-tropomyosin removal and reconstitution 2012 Beatrice Scellini; Claudia Ferrara; Nicoletta Piroddi; John Sumida; Corrado Poggesi; Sherwin S. Lehrer; Chiara Tesi