We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.

Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-Year survival / Nenna, R; Midulla, F; Masi, L; Bacci, GIACOMO MARIA; Frassanito, Anna; Baggi, R; Brandi, MARIA LUISA; Avenali, S; Mirabile, L; Serio, P.. - In: INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY. - ISSN 1872-8464. - ELETTRONICO. - 99:(2017), pp. 13-16. [10.1016/j.ijporl.2017.05.008]

Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-Year survival.

BACCI, GIACOMO MARIA;FRASSANITO, ANNA;BRANDI, MARIA LUISA;
2017

Abstract

We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.
2017
99
13
16
Nenna, R; Midulla, F; Masi, L; Bacci, GIACOMO MARIA; Frassanito, Anna; Baggi, R; Brandi, MARIA LUISA; Avenali, S; Mirabile, L; Serio, P.
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Utilizza questo identificatore per citare o creare un link a questa risorsa: https://hdl.handle.net/2158/1095087
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