PIONER, JOSE' MANUEL

PIONER, JOSE' MANUEL  

Biologia  

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Risultati 1 - 20 di 37 (tempo di esecuzione: 0.067 secondi).
Titolo Data di pubblicazione Autore(i) File
A Novel Method of Isolating Myofibrils From Primary Cardiomyocyte Culture Suitable for Myofibril Mechanical Study 2019 Woulfe, Kathleen C; Ferrara, Claudia; Pioner, Jose Manuel; Mahaffey, Jennifer H; Coppini, Raffaele; Scellini, Beatrice; Ferrantini, Cecilia; Piroddi, Nicoletta; Tesi, Chiara; Poggesi, Corrado; Jeong, Mark
Absence of full-length dystrophin impairs normal maturation and contraction of cardiomyocytes derived from human induced pluripotent stem cells 2019 Pioner, J. M.; Guan, Xuan; Klaiman, Jordan M; Racca, Alice W; Pabon, Lil; Muskheli, Veronica; Macadangdang, Jesse; Ferrantini, Cecilia; Hoopmann, Michael R; Moritz, Robert L; Kim, Deok-Ho; Tesi, Chiara; Poggesi, Corrado; Murry, Charles E; Childers, Martin K; Mack, David L; Regnier, Michael
Advanced Morpho-Functional Analysis on Ventricular and Atrial Tissue Reveals Cross-Bridge Kinetics Alterations and Sarcomere Energetic Impairment in Hcm Patients 2019 Vitale, G; Lazzeri, E; Costantini, I; Giardini, F; Mazzamuto, G; Crocini, C; Piroddi, N; Scellini, B; Pioner, JM; Ferrantini, C; Tesi, C; Pavone, FS; Sacconi, L; Poggesi, C
Advances in Stem Cell Modeling of Dystrophin-Associated Disease: Implications for the Wider World of Dilated Cardiomyopathy 2020 Pioner JM, Fornaro A, Coppini R, Ceschia N, Sacconi L, Donati MA, Favilli S, Poggesi C, Olivotto I, Ferrantini C
Atrial Remodeling in Hypertrophic Cardiomyopathy 2017 Ferrantini, Cecilia; Pioner, Josè Manuel; Gentile, Francesca; Coppini, Raffaele; Morelli, Cristina; Piroddi, Nicoletta; Scellini, Beatrice; Cerbai, Elisabetta; Tardiff, Jil; Tesi, Chiara; Olivotto, Iacopo; Poggesi, Corrado
Calcium handling maturation and adaptation to increased substrate stiffness in human iPSC-derived cardiomyocytes: The impact of full-length dystrophin deficiency 2022 Pioner, J.M.; Santini, Lorenzo; Palandri, Chiara; Langione, Marianna; Grandinetti, Bruno; Querceto, Silvia; Martella, Daniele; Mazzantini, Costanza; Scellini, Beatrice; Giammarino, Lucrezia; Lupi, Flavia; Mazzarotto, Francesco; Gowran, Aoife; Rovina, Davide; Santoro, Rosaria; Pompilio, Giulio; Tesi, Chiara; Parmeggiani, Camilla; Regnier, Michael; Cerbai, Elisabetta; Mack, David L.; Poggesi, Corrado; Ferrantini, Cecilia; Coppini, Raffaele
Contractile properties of developing human fetal cardiac muscle 2016 Alice W. Racca, Jordan M. Klaiman, Josè Manuel Pioner, Yuanhua Cheng, Anita E. Beck, Farid Moussavi-Harami, Michael J. Bamshad, Michael Regnier
Contraction and electrophysiological abnormalities in myofilament mutation-positive and mutation-negative human HCM myocardium 2022 Pioner, Jose' Manuel; Vitale, Giulia; Santini, Lorenzo; Palandri, Chiara; Bueno-Orovio, Alfonso; Margara, Francesca; Piroddi, Nicoletta; Scellini, Beatrice; Tesi, Chiara; Coppini, Raffaele; Ferrantini, Cecilia; Poggesi, Corrado
Design of Biocompatible Liquid Cristal Elastomers Reproducing the Mechanical Properties of Human Cardiac Muscle 2019 Ferrantini, C; Pioner, JM; Martella, D; Coppini, R; Piroddi, N; Paoli, P; Calamai, M; Pavone, FS; Wiersma, D; Tesi, C; Cerbai, E; Poggesi, C; Sacconi, L; Parmeggiani, C
Design of muscle contraction assist devices by liquid crystalline elastomers 2018 Cecilia Ferrantini , José Manuel Pioner, Daniele Martella, Raffaele Coppini, Nicoletta Piroddi, Francesco Saverio Pavone, Diederik Sybolt Wiersma, Chiara Tesi, Elisabetta Cerbai, Corrado Poggesi, Leonardo Sacconi, Camilla Parmeggiani
Development of Light-Responsive Liquid Crystalline Elastomers to Assist Cardiac Contraction 2019 Ferrantini, Cecilia; Pioner, Josè Manuel; Martella, Daniele; Coppini, Raffaele; Piroddi, Nicoletta; Paoli, Paolo; Calamai, Martino; Pavone, Francesco; Wiersma, Diederik Sybolt; Tesi, Chiara; Cerbai, Elisabetta; Poggesi, Corrado; Sacconi, Leonardo; Parmeggiani, Camilla
EFFECTS OF MAVACAMTEN, A FIRST-IN-CLASS INHIBITOR OF SARCOMERIC MYOSINS, ON THE MECHANICS OF ATRIAL AND VENTRICULAR MAMMALIAN MYOCARDIUM AND FAST SKELETAL MUSCLE 2022 Beatrice Scellini, Nicoletta Piroddi , Marica Dente , Giulia Vitale , Josè Manuel Pioner , Raffaele Coppini , Cecilia Ferrantini , Corrado Poggesi , Chiara Tesi
Electrophysiological and Contractile Effects of Disopyramide in Patients With Obstructive Hypertrophic Cardiomyopathy: a Translational Study 2019 Coppini, Raffaele; Ferrantini, Cecilia; Pioner, Josè Manuel; Santini, Lorenzo; Wang, Zhinuo J.; Palandri, Chiara; Scardigli, Marina; Vitale, Giulia; Sacconi, Leonardo; Stefàno, Pierluigi; Flink, Laura; Riedy, Katherine; Pavone, Francesco Saverio; Cerbai, Elisabetta; Poggesi, Corrado; Mugelli, Alessandro; Bueno-Orovio, Alfonso; Olivotto, Iacopo; Sherrid, Mark V.
Full-length dystrophin deficiency leads to contractile and calcium transient defects in human engineered heart tissues 2022 Bremner, Samantha B; Mandrycky, Christian J; Leonard, Andrea; Padgett, Ruby M; Levinson, Alan R; Rehn, Ethan S; Pioner, JM; Sniadecki, Nathan J; Mack, David L
Genotype-Driven Pathogenesis of Atrial Fibrillation in Hypertrophic Cardiomyopathy: The Case of Different TNNT2 Mutations 2022 Josè Manuel Pioner, Giulia Vitale, Francesca Gentile, Beatrice Scellini, Nicoletta Piroddi, Elisabetta Cerbai, Iacopo Olivotto, Jil Tardiff, Raffaele Coppini, Chiara Tesi, Corrado Poggesi, Cecilia Ferrantini
Impact of E163R cTnT mutation on cardiac mechanics and energetics in a murine model 2014 Tosi B.; Ferrantini C.; Pioner JM; Ferrara C.; Scellini B.; Piroddi N.; Abdullah S.; Raffaele C.; Bardi S.; Tardiff J.; Tesi C.; Poggesi C.
IPSC derived cardiac fibroblasts of DMD patients show compromised actin microfilaments, metabolic shift and pro-fibrotic phenotype 2023 Soussi, Salwa; Savchenko, Lesia; Rovina, Davide; Iacovoni, Jason S; Gottinger, Andrea; Viallettes, Maxime; Pioner, J.M.; Farini, Andrea; Mallia, Sara; Rabino, Martina; Pompilio, Giulio; Parini, Angelo; Lairez, Olivier; Gowran, Aoife; Pizzinat, Nathalie
Isolation and Mechanical Measurements of Myofibrils from Human Induced Pluripotent Stem Cell-Derived Cardiomyocytes. 2016 Pioner, Jm; Racca, Aw; Klaiman, Jm; Yang, Kc; Guan, X; Pabon, L; Muskheli, V; Zaunbrecher, R; Macadangdang, J; Jeong, My; Mack, Dl; Childers, Mk; Kim, Dh; Tesi, C; Poggesi, C; Murry, Ce; Regnier, M
Late sodium current inhibitors to treat exercise induced obstruction in hypertrophic cardiomyopathy: an in vitro study in human myocardium. 2018 Cecilia Ferrantini, Josè Manuel Pioner, Luca Mazzoni, Francesca Gentile, Benedetta Tosi, Alessandra Rossi, Luiz Belardinelli, Chiara Tesi, Chiara Palandri, Rosanna Matucci, Elisabetta Cerbai, Iacopo Olivotto, Corrado Poggesi, Alessandro Mugelli, Raffaele Coppini
Liquid Crystalline Networks toward Regenerative Medicine and Tissue Repair 2017 Martella, Daniele; Paoli, Paolo; Pioner, JOSE' MANUEL; Sacconi, Leonardo; Coppini, Raffaele; Santini, Lorenzo; Lulli, Matteo; Cerbai, Elisabetta; Wiersma, DIEDERIK SYBOLT; Poggesi, Corrado; Ferrantini, Cecilia; Parmeggiani, Camilla